Tumor juga lebih sering meluas ke arah sinus sphenoid dan agak jarang ke arah sinus. Nasopharyngeal angiofibroma definition of nasopharyngeal. Well circumscribed but unencapsulated polypoid fibrous mass, bleeds severely on manipulation and biopsy, may occlude nares. Nasopharyngeal angiofibroma introduction juvenile nasopharyngeal angiofibroma jna is a benign, but locally aggressive and extremely vascular head and neck neoplasm, occurring almost exclusively in the nasopharynx of adolescent males. Juvenile nasopharyngeal angiofibromas jna are a rare benign, but locally aggressive, vascular tumor. Doc lapsus angiofibroma nasofaring anggy novitasari. Introduction uncommon, benign and extremely vascular tumour up to 0. Angiofibroma nasofaring juvenile free download as pdf file. It is the most common benign tumor of the nasopharnyx but only accounts for less than 0. A juvenile nasopharyngeal angiofibroma with an unusual. Juvenile nasopharyngeal angiofibroma with orbital extension.
Jul 15, 2015 juvenile nasopharyngeal angiofibroma jna is a benign neoplasm of the nasopharynx. Juvenile nasopharyngeal angiofibromas are a rare benign, but locally aggressive, vascular tumors that occur almost exclusively in young men on imaging, they present as a vividly enhancing softtissue masses centered on the sphenopalatine foramen. The bilateral selective angiograms of the external carotid arteries as well as of the internal carotid arteries revealed a distinct tumor stain. In the general population, jna occurs at an incidence of roughly 1. A juvenile nasopharyngeal angiofibroma jna is a noncancerous tumor made up of blood vessels that grow at the posterior aspect of the nose. Intricate mixture of stellate and staghorn blood vessels with variable vessel wall thickness ranging from single layer of endothelium to variable smooth muscle coat.
Juvenile nasopharyngeal angiofibroma jna is a histologically benign vascular tumor that arises in boys between the ages of 12 and 15 years, with only rare cases reported in patients younger than 10 or older than 25. Juvenile nasopharyngeal angiofibroma with orbital extension angiofibroma nasofaringeo juvenil con extension orbitaria. Juvenile nasopharyngeal angiofibroma is tumour almost exclusively seen in adolescent males, constituting less than 1% of all neoplasms in. Sinus tomography reports osteolytic lesion of the left nostril, nasopharynx and pterygopalatine fossa. Magnetic resonance imaging findings ayse gul alimli, murat ucar, cigdem oztunali, koray akkan, oznur boyunaga, cagr. Juvenile nasopharyngeal angiofibroma a free powerpoint ppt presentation displayed as a flash slide show on id. A male, 21 years of age, without relevant history, presented with left exophthalmos and diplopia in extreme gaze positions with 2 weeks evolution, without clinic of epistaxis or nasal obstruction. Nasopharyngeal angiofibroma is a benign, vascular, polypoid fibrous mass in located in the the posterolateral wall of the nasal cavity. Surgery combined with preoperative embolization has been the treatment of choice for jna patients. It is a rare, benign, vascular neoplasm that accounts for less than 0. Abstrak angiofibroma nasofaring adalah tumor jinak nasofaring yang secara histopatologis merupakan tumor jinak, tetapi secara klinis bersifat destruktif. Although the exact pathogenesis of the tumour is not yet known, natural history and growth patterns can be predicted.
Juvenile nasopharyngeal angiofibroma jna is a rare tumor that predominantly occurs in adolescent males, the average age of occurence being 15. Pdf juvenile nasopharyngeal angiofibroma in a tertiary centre. Juvenile nasopharyngeal angiofibroma electronic journal of. Juvenile nasopharyngeal angiofibroma jna is an uncommon, benign tumor of the nose that is generally seen in boys. Although the exact pathogenesis of the tumour is not yet known, natural history.
The pictures used in this presentation have been obtained from a number of sources. A case of a juvenile nasopharyngeal angiofibroma is reported. Jan 08, 2018 javier and his family share their experience at johns hopkins medicine, after seeking treatment following a diagnosis of a juvenile nasopharyngeal angiofibroma jna tumor. Juvenile nasopharyngeal angiofibroma j na adalah operasi. We report the case of a 17yearold male who presented in 1995 with a mass filling the left posterior nasal cavity. Juvenile nasopharyngeal angiofibroma jna is a relatively rare tumor of the nasopharynx, comprising only 0. Although rare cases have been reported in females, the tumor has such a strong male. Radiologists prior knowledge on the tumors characteristics aids in establishing a diagnosis. Typical signs are nasal and eustachian tube obstruction, adenoidal speech, and dysphagia. Nasoangiofibroma youth is a highly vascularized tumor almost exclusively male adolescents presentation.
However, the extensions of the tumor seem to be independent, each one with distinct behavior. Mar 07, 2020 it most commonly affects adolescent males and may grow into fissures of the. Juvenile nasopharyngeal angiofibromas are benign but highly vascular tumors. Review article nasopharyngeal angiofibroma ashutosh hota. Infact hippocrates goes on to describe a polyp in the nose which weeped blood. Females with juvenile nasopharyngeal angiofibroma jna should undergo genetic testing. The study was approved by the institutional ethical committee. Although the use of nonsurgical therapies is described in the literature, surgery is currently considered the ideal treatment for. Angiofibroma nasofaring belia pdf juvenile nasopharyngeal angiofibroma is a pathologically benign yet locally aggressive and destructive vascular lesion of head and neck. Ppt juvenile nasopharyngeal angiofibroma powerpoint. Jnas originate from the posterior choanal tissues and rapidly extend into the surrounding regions, including the nasopharynx, the orbits, and even the intracranial cavity. It most commonly affects adolescent males and may grow into fissures of the. Oct 18, 2018 juvenile nasopharyngeal angiofibroma jna is an uncommon, benign tumor of the nose that is generally seen in boys.
Please choose whether or not you want other users to be able to see on your profile that deuss library is a favorite of yours. Although the use of nonsurgical therapies is described in the literature, surgery is currently considered the ideal. Two types of lateral extension in juvenile nasopharyngeal. Juvenile nasopharyngeal angiofibroma has been documented since the time of hippocrates 4 bc. Juvenile nasopharyngeal angiofibroma jna javiers story. Pdf this is a retrospective study that aimed to examine the outcomes of patients presenting with juvenile nasopharyngeal angiofibroma jna at a. Given its vascularity, prominent flow voids are seen on mri leading to a salt and pepper appearance. We had recently a case of an extensive jna in the r nasal cavity extending from the anterior nares to the nasopharynx involving the rt pterygopalatine. May 16, 2018 nasopharyngeal angiofibroma is usually encapsulated and composed of vascular tissue and fibrous stroma with coarse or fine collagen fibers. The importance of selective angiography in cases of surmised juvenile nasopharyngeal angiofibromas is emphasized, since this examination makes it.
It most commonly affects adolescent males because it is a hormonesensitive tumor. Case report endoscopic excision of juvenile nasopharyngeal. This is a classical presentation of juvenile nasopharyngeal angiofibroma. Juvenile nasopharyngeal angiofibroma jna is a rare, benign, but locally aggressive tumor occurring almost exclusively in adolescent males. The most common presenting symptom is painless nasal obstruction or epistaxis.
Sinonasnasopharyngeal angiofibroma juvenile with subsequent. Juvenile nasopharyngeal angiofibroma is a rare benign tumour of vascular origin found in adolescent males, originating around the sphenopalatine foramen. Juvenile nasopharyngeal angiofibroma jna onset most commonly is in the second decade. The records of 37 patients with tumors extending laterally from the nasopharynx were included in the study. We aimed to report the characteristic magnetic resonance imaging mri findings and the spread patterns of jna. Nasopharyngeal angiofibroma is usually encapsulated and composed of vascular tissue and fibrous stroma with coarse or fine collagen fibers.
Juvenile nasopharyngeal angiofibroma jna is rare in patients older than 25 years. Jul 22, 2019 angiofibroma nasofaring belia pdf juvenile nasopharyngeal angiofibroma is a pathologically benign yet locally aggressive and destructive vascular lesion of head and neck. Juvenile angiofibroma is a noncancerous growth that causes bleeding in the nose and sinuses. They often grow quickly during puberty, then slow down or. Juvenile nasopharyngeal angiofibromas occur almost exclusively in males and usually in adolescence 15 years. The importance of selective angiography in cases of surmised juvenile nasopharyngeal angiofibromas is emphasized, since this examination makes it possible for one to determine not only the.
Nasopharyngeal angiofibroma an overview sciencedirect. Bedah sinonasal endoskopik angiofibroma nasofaring belia. Nasopharyngeal angiofibroma symptoms aurora health care. Their use is purely for academic and teaching purposes. Hmm, seems to be two editions of this book with separate book pages. Adolescents and young adults between 14 and 25 years are affected, and there is a distinct male predominance. Vessels are thinwalled, lack elastic fibers, have absent or incomplete smooth muscle, and vary in appearance from stellate or staghorn to barely conspicuous because of stromal compression. Tumor ini sering terjadi pada lakilaki prepubertas dan remaja, jarang ditemukan pada pasien. Jna berasal dari posterolateral nasofaring di daerah fossa pterygopallatine.
These tumors are benign, however they are locally invasive. It is almost exclusicely encountered in adolescent males 1. Ppt journal juvenile nasopharynx angiofibroma free download as powerpoint presentation. Juvenile nasopharyngeal angiofibroma presenting as a. Juvenile nasopharyngeal angiofibroma jna is a rare tumor that exhibits a predictable spreading pattern. Juvenile nasopharyngeal angiofibroma is a rare, benign tumor that occurs most often in adolescent males. Jnas occur almost exclusively in the nasopharynx of adolescent. Jna biasanya selalu meluas melalui foramen sphenopallatine, meliputi fossa pterygopallatine dan cavum nasal posterior. Juvenile nasopharyngeal angiofibroma, angiofibroma nasofaring juvenil, radioterapi, tumor jinak. Juvenile nasopharyngeal angiofibroma with audio youtube. Javier and his family share their experience at johns hopkins medicine, after seeking treatment following a diagnosis of a juvenile nasopharyngeal angiofibroma jna tumor. Common practice is to excise the tumor with open or endoscopic surgery. The tumor is locally aggressive and can invade into surrounding structures and cause significant complications.
Molecular pathogenesis of juvenile nasopharyngeal angiofibroma in brazilian patients. Juvenile nasopharyngeal angiofibroma jna represents. Visual acuity was 2020 in both eyes and intraocular pressure iop 24 mmhg in left eye le without limitations in ocular movement. Juvenile nasopharyngeal angiofibroma radiology reference. May 05, 20 greetings from gv ent centre, kochi, india. Juvenile nasopharyngeal angiofibroma presenting as a facial. Shaheen in 1930 reported the first female patient with juvenile nasopharyngeal. Ppt journal juvenile nasopharynx angiofibroma radiation. Juvenile nasopharyngeal angiofibroma knowledge for medical. Sep 01, 2008 juvenile nasopharyngeal angiofibroma is a rare, benign tumor that occurs most often in adolescent males. It is an aggressive neoplasm and shows a propensity for destructive local spread often extending to the base of. Juvenile nasopharyngeal angiofibroma jna is a rare, benign, and highly vascular and locally aggressive tumor that accounts for 0.
Juvenile nasopharyngeal angiofibroma 420 introduction juvenile nasopharyngeal angiofibroma jna represents 0. Juvenile nasopharyngeal angiofibroma jna is an uncommon tumor of the sphenopalatine foramen. Juvenile nasopharyngeal angiofibroma jna is a benign tumor that tends to bleed and occurs in the nasopharynx of prepubertal and adolescent males. Juvenile nasopharyngeal angiofibroma knowledge for. The juvenile nasopharyngeal angiofibroma has a characteristic growth in all directions from its origin. Juvenile nasopharyngeal angiofibroma is a locally aggressive benign vascular neoplasm, composed of vasogenic and myofibroblastic elements, accounts for 0. They often grow quickly during puberty, then slow down or stop growing entirely after adolescence. Juvenile angiofibroma is a rare benign lesion originating from the pterygopalatine fossa with distinctive epidemiologic features and growth patterns. Juvenile nasopharyngeal angiofibroma jna is a rare benign tumor arising predominantly in the nasopharynx of adolescent males. This is a histologically benign lesion with very aggressive local behavior. The tumor usually arises in puberty and is more common in boys than in girls.
The typical patient is an adolescent male with a clinical history of recurrent epistaxis and nasal obstruction. In 1906 chareau revived the interest in the study of juvenile nasopharyngeal angiofibroma. Juvenile nasopharyngeal angiofibroma radiology case. The tumor contains many blood vessels and spreads within the area in which it started locally invasive. Pdf juvenile nasopharyngeal angiofibroma researchgate. Review article nasopharyngeal angiofibroma ashutosh hota s. May 16, 2018 juvenile nasopharyngeal angiofibroma jna occurs exclusively in males. Jun 28, 2019 angiofibroma nasofaring belia pdf juvenile nasopharyngeal angiofibroma is a pathologically benign yet locally aggressive and destructive vascular lesion of head and neck.
915 1024 683 347 611 895 784 69 1236 756 384 494 448 359 10 1414 1520 1560 674 574 1386 333 1342 818 930 1496 1276 928 1205 281 983 22 405 1465 1467 676 644 1090 1381 211 1181